Concept Map cysitc Fibrosis PDF

Preview

Summary

Practice Material for pediatrics of nursing BSN program ....

Description

Pathophysiology of cystic fibrosis and drugs used in associated digestive tract diseases 1 Physiopathology of the disease: overall symptoms. 2 Gastrointestinal disease. In CF patients gastrointestinal symptoms, such as nausea, vomiting,... 3 Pancreatic disease. The pancreas is one of the main organs affected by dysfunction of the CFTR.

Persistent cough with phlegm Postnasal drip Salty tasting skin Wheezing Shortness of breath Sinusitis

Monitor respiratory and heart rate for any changes.

Assess for changes in respiratory status such as cyanosis, pallor, changes in the level of consciousness, labored breathing and tachypnea.

Cystic Fibrosis

Cystic fibrosis (CF) is an inherited disorder that causes severe damage to the lungs, digestive system and other organs in the body. Cystic fibrosis affects the cells that produce mucus, sweat and digestive juices. These secreted fluids are normally thin and slippery.

Impaired Gas Exchange

Ineffective Airway Clearance

Assess cough for effectiveness. Assess respiratory rate, work of breathing, use of accessory muscles, and the presence of retractions.

Monitor transcutaneous carbon dioxide as ordered.

Imbalanced Nutrition: Less Than Body Requirements

Assess the abdomen for bloating, fullness, bowel sounds, or palpable stool mass. Monitor stool patterns for frequency, odor, consistency, and the presence of oil or grease. Assess the skin’s color, integrity, and turgor.

Assess the chest wall for even chest expansion. Monitor for excessive thirst, urination, and hunger. Obtain bedside blood glucose readings as ordered....